Congenital nasal pyriform aperture stenosis repair: A case series and discussion of postoperative care

Congenital nasal pyriform aperture stenosis (CNPAS) is a rare condition related to holoprosencephaly in which bony overgrowth of the medial process maxilla narrows aperture. CNPAS presents neonates with signs upper airway obstruction ranging from mild severe respiratory distress and failure thrive. Surgical intervention indicated after failed conservative measures generally includes temporary stent placement. We report series 3 cases treated surgically, examine postoperative care recommendations literature, present comprehensive regimen novel method maintain patency.